4A44
Vasculitis
Vasculite
CategoryDefinition
Vasculitides represent a heterogenous group of diseases of multifactorial aetiology characterised by inflammatory lesions of vessels. These lesions consist of fibrinoid necrosis (necrotizing arteritis), giant cell infiltration without necrosis, immunoglobulins deposit or leukocytoclastic infiltration. The spectrum and severity of the systemic vaculitides is broad, from life or sight threatening fulminant disease to relatively minor skin disease.
Subcategories (12)
4A44.0Rhizomelic pseudopolyarthritis4A44.1Aortic arch syndrome4A44.2Giant cell arteritis4A44.3Single organ vasculitis4A44.4Polyarteritis nodosa4A44.5Mucocutaneous lymph node syndrome4A44.6Sneddon syndrome4A44.7Primary angiitis of the central nervous system4A44.8Thromboangiitis obliterans4A44.9Immune complex small vessel vasculitis4A44.AAntineutrophil cytoplasmic antibody-associated vasculitis4A44.BLeukocytoclastic vasculitis