4A44.A
Antineutrophil cytoplasmic antibody-associated vasculitis
Vasculite associada aos anticorpos anticitoplasma de neutrófilos
CategoryDefinition
Necrotizing vasculitis, with few or no immune deposits, predominantly affecting small vessels (i.e., capillaries, venules, arterioles and small arteries), associated with MPO-ANCA or PR3-ANCA. Not all patients have ANCA. Add a prefix indicating ANCA reactivity, e.g. PR3-ANCA, MPO-ANCA, ANCA-negative.